Palabras clave
Síndrome de Ascher; Doble labio
Cómo citar
Síndrome de Ascher.: Clinica y tratamiento a propósito de un caso clínico. (2018). Odontoestomatología, 20(31). https://www.odon.edu.uy/ojs/index.php/ode/article/view/263
Resumen
Presentamos un paciente con “Sindrome de Ascher”. Se trata de una rara entidad benigna, que es una anomalía congénita o adquirida de etiología desconocida. Clínicamente el Síndrome de Ascher, está compuesto por una tríada de signos clínicos: doble labio (siendo el superior el más frecuentemente involucrado), blefarocalasia y bocio no tóxico (agrandamiento tiroideo, no funcional y ausente en aproximadamente la mitad de los casos). Cuando la deformidad labial interfiere con la masticación o provoca groseras alteraciones estéticas, el tratamiento quirúrgico está indicado.
Referencias
1. Cortes-Aroche S. Labio doble tratado con incisión en media luna. Presentación de un caso. Rev. Med. Inst.Mex.Seguro Soc. 2007; 45(3):277-80. [ Links ]
2. Kara IG, Kara CO. Ascher syndrome. Otolaryngol. Head Neck Surg. 2001;124(2):236-7. [ Links ]
3. Gorlin RJ, Cohen MM, Levin LS, eds. Syndromes of the head and neck. 3rd. Ed. New York: Oxford University Press.1990;p.420-1 [ Links ]
4. Gomez - Duaso AJ, Seoane J, Vazquez- Garcia J, Arjona C. Ascher Syndrome: report of two cases. J Oral Maxillofac Surg. 1981;34:31-4. [ Links ]
5. Ascher KW. Blepharochalasis mit struma und doppellippe. Klinische Monatsbl Augenheilkd 1920;65:86-97. [ Links ]
6. Ascher KW. Das syndrom blepharochalasis, struma und doppellippe kiln. En: Gorlin RJ, Pindborg JJ, editors Syndromes of the head and neck. New York: McGraw- Hill;1964.p.2287-88 [ Links ]
7. Barnett ML, Bossahardt LL, Morgan F. Double lip and doble lip with blepharochalasis (Ascher's syndrome). Oral Surg.1972; 34:727. [ Links ]
8. Alkan A, Metin M. Maxillary double lip: Report of two cases. J Oral Surg. 2001;4369-72. [ Links ]
9. Laffler WB. Blepharochalasis: Report of a case this trophoneurosis involving also the upper lip. Cleveland Med. J. 1909;8:131-35. [ Links ]
10. Gomez-Duaso AJ, Seoane J, Vázquez-Garcia J, Arjona C. Sindrome de Ascher reporte de dos casos. J Oral Maxillofac Surg. 1997 Jan.; 55(1): 88-90. [ Links ]
11. Costa-Hanemann JA, et all: Labio doble congénito asociado a hemangiomas: a propósito de un caso. Med. Oral 2004;9:155-8 [ Links ]
12. Gilvani AOC, et all: Síndrome de Ascher: aspectos clínicos y terapéuticos desta rara deformidade da face. Rev. Bras. Cir. Craniomaxilofac. 2008;11(3):116-8. [ Links ]
13. Dalmau J, Puig L, Huevas E, Peramiquel L, Pimentel CL, Alomar A. Blepharochalasia y dos labios: diagnóstico y tratamiento del síndrome de Ascher. J. Eur. Acad Dermatol Venereol. 2006 Nov; 20 (10):1390-1. [ Links ]
14. Reddy KA, Roa AK. A congenital double lip: a review of seven cases. Plast Reconstru. Surg. 1989, 84(3):420-3 [ Links ]
15. Lebuisson D, Leroy L, Aron JJ, Jeaneau E, J. Guillard J P. Síndrome de Laffer-Ascher. Ophtalmol . 1978 Dec. 1 (12) :751-2. [ Links ]
16. Ali K. Ascher syndrome: a case report and review of the literature. Oral surg Oral Med Oral Pathol Oral Radiol. Endod. 2007;103(2):26-8. [ Links ]
17. Franceschetti A. Manifestation the blepharochalasis chez de pére associé á double lévre apparaissant également chez sa fillette agée dún mois. J. Genet Hum. 1955;4:181-2 [ Links ]
18. Narang R. Double lip due to injury. A case report. J Indian Dent Assoc. 1970;42(4):112-3. [ Links ]
19. Rintala AE. Congenital double lip Ascher syndrome: Relationship to the lower lip sinus syndrome. Br J Plast surg 1981; 34:31-4. [ Links ]
20. Swerdloff G. Double lip report of a case. Oral surg Oral Med Oral Pathol. 1960;15:627-9. [ Links ]
21. Dingman RO, Billman H. Double Lip. J Oral Surg 1947; 5: 146-148 [ Links ]
22. Reddy KA, Kotewara A Congenital double lip: a review of seven cases. Plast Reconstr Surg. 1988; 84:420 [ Links ]
23. Dorrance GM. Double Lip Ann Surg 1922 [ Links ]
24. Guerrero Santos J. Altamirano JT, The use of W- plasty for the correction of double lyp deformity. Plast Reconstr Surg 1967; 39:478 [ Links ]
25. Lamster l.B. Mucosal reducción for correction of a maxillary double lip. Report of case. Oral Surg Oral Med Oral Pathol 1983; 55(5) :457-458 [ Links ]
26. Eski M., Nisanci M., Aktas A., Sengezer M. Congenital double lip: review of 5 cases. Br. J. Oral Maxillofac. Surg. 2007;45:68-70. [ Links ]
27. Beinhoff U, Piza-Katzer H. Double lip in a patient with Ascher´s syndrome. Eur. J. Plast Surg.1998;21(7):370-3. [ Links ]
28. Alkan A, Metin M. Doble labio maxilar: presentación de dos casos. J Oral Sci . 2001 Mar; 43 (1):69-72. [ Links ]
29. Chander R, Mal J, Jain A, Jaykar K. Ascher Syndrome: A Case Report. Pediatr. Dermatol. 2009 Sep-Oct; 26 (5) :631-3 [ Links ]
30. Atzeni M, Ceratola E, Zaccheddu E, Manca A, Saba L, Ribuffo D. Corrección quirúrgica y la RM de doble labio en el síndrome de Ascher: registro de un caso y revisión de la literatura. Eur Rev Med Sci. Pharmacol. 2009 Jul-Aug; 13 (4):309. [ Links ]
2. Kara IG, Kara CO. Ascher syndrome. Otolaryngol. Head Neck Surg. 2001;124(2):236-7. [ Links ]
3. Gorlin RJ, Cohen MM, Levin LS, eds. Syndromes of the head and neck. 3rd. Ed. New York: Oxford University Press.1990;p.420-1 [ Links ]
4. Gomez - Duaso AJ, Seoane J, Vazquez- Garcia J, Arjona C. Ascher Syndrome: report of two cases. J Oral Maxillofac Surg. 1981;34:31-4. [ Links ]
5. Ascher KW. Blepharochalasis mit struma und doppellippe. Klinische Monatsbl Augenheilkd 1920;65:86-97. [ Links ]
6. Ascher KW. Das syndrom blepharochalasis, struma und doppellippe kiln. En: Gorlin RJ, Pindborg JJ, editors Syndromes of the head and neck. New York: McGraw- Hill;1964.p.2287-88 [ Links ]
7. Barnett ML, Bossahardt LL, Morgan F. Double lip and doble lip with blepharochalasis (Ascher's syndrome). Oral Surg.1972; 34:727. [ Links ]
8. Alkan A, Metin M. Maxillary double lip: Report of two cases. J Oral Surg. 2001;4369-72. [ Links ]
9. Laffler WB. Blepharochalasis: Report of a case this trophoneurosis involving also the upper lip. Cleveland Med. J. 1909;8:131-35. [ Links ]
10. Gomez-Duaso AJ, Seoane J, Vázquez-Garcia J, Arjona C. Sindrome de Ascher reporte de dos casos. J Oral Maxillofac Surg. 1997 Jan.; 55(1): 88-90. [ Links ]
11. Costa-Hanemann JA, et all: Labio doble congénito asociado a hemangiomas: a propósito de un caso. Med. Oral 2004;9:155-8 [ Links ]
12. Gilvani AOC, et all: Síndrome de Ascher: aspectos clínicos y terapéuticos desta rara deformidade da face. Rev. Bras. Cir. Craniomaxilofac. 2008;11(3):116-8. [ Links ]
13. Dalmau J, Puig L, Huevas E, Peramiquel L, Pimentel CL, Alomar A. Blepharochalasia y dos labios: diagnóstico y tratamiento del síndrome de Ascher. J. Eur. Acad Dermatol Venereol. 2006 Nov; 20 (10):1390-1. [ Links ]
14. Reddy KA, Roa AK. A congenital double lip: a review of seven cases. Plast Reconstru. Surg. 1989, 84(3):420-3 [ Links ]
15. Lebuisson D, Leroy L, Aron JJ, Jeaneau E, J. Guillard J P. Síndrome de Laffer-Ascher. Ophtalmol . 1978 Dec. 1 (12) :751-2. [ Links ]
16. Ali K. Ascher syndrome: a case report and review of the literature. Oral surg Oral Med Oral Pathol Oral Radiol. Endod. 2007;103(2):26-8. [ Links ]
17. Franceschetti A. Manifestation the blepharochalasis chez de pére associé á double lévre apparaissant également chez sa fillette agée dún mois. J. Genet Hum. 1955;4:181-2 [ Links ]
18. Narang R. Double lip due to injury. A case report. J Indian Dent Assoc. 1970;42(4):112-3. [ Links ]
19. Rintala AE. Congenital double lip Ascher syndrome: Relationship to the lower lip sinus syndrome. Br J Plast surg 1981; 34:31-4. [ Links ]
20. Swerdloff G. Double lip report of a case. Oral surg Oral Med Oral Pathol. 1960;15:627-9. [ Links ]
21. Dingman RO, Billman H. Double Lip. J Oral Surg 1947; 5: 146-148 [ Links ]
22. Reddy KA, Kotewara A Congenital double lip: a review of seven cases. Plast Reconstr Surg. 1988; 84:420 [ Links ]
23. Dorrance GM. Double Lip Ann Surg 1922 [ Links ]
24. Guerrero Santos J. Altamirano JT, The use of W- plasty for the correction of double lyp deformity. Plast Reconstr Surg 1967; 39:478 [ Links ]
25. Lamster l.B. Mucosal reducción for correction of a maxillary double lip. Report of case. Oral Surg Oral Med Oral Pathol 1983; 55(5) :457-458 [ Links ]
26. Eski M., Nisanci M., Aktas A., Sengezer M. Congenital double lip: review of 5 cases. Br. J. Oral Maxillofac. Surg. 2007;45:68-70. [ Links ]
27. Beinhoff U, Piza-Katzer H. Double lip in a patient with Ascher´s syndrome. Eur. J. Plast Surg.1998;21(7):370-3. [ Links ]
28. Alkan A, Metin M. Doble labio maxilar: presentación de dos casos. J Oral Sci . 2001 Mar; 43 (1):69-72. [ Links ]
29. Chander R, Mal J, Jain A, Jaykar K. Ascher Syndrome: A Case Report. Pediatr. Dermatol. 2009 Sep-Oct; 26 (5) :631-3 [ Links ]
30. Atzeni M, Ceratola E, Zaccheddu E, Manca A, Saba L, Ribuffo D. Corrección quirúrgica y la RM de doble labio en el síndrome de Ascher: registro de un caso y revisión de la literatura. Eur Rev Med Sci. Pharmacol. 2009 Jul-Aug; 13 (4):309. [ Links ]